top of page
Writer's pictureKate

A Rare Genetic Mutation (as published on The Firefly Sisterhood)

Updated: Jul 11, 2019

Click here to see my guest blog post on The Firefly Sisterhood's website. Or, read below.


 

Breast cancer may have saved my life. I say “may have” on purpose because I recently received the call from my doctor with my upper endoscopy and stomach biopsy pathology results. Out of the ninety-two biopsies taken during my stomach mapping procedure, one came back positive for signet ring cells. These cells are common in the stomachs of people with the rare genetic mutation Cadherin 1 (CDH1),which I was diagnosed with earlier this year. This means there are cancerous cells in the lining of my stomach as I write this.


Let me give you some background information to put this all into context. I was diagnosed with Stage 3 Invasive Lobular Carcinoma of the left breast about ten months ago, at the age of thirty two. Because my mom was also diagnosed with breast cancer at a very young age, I was at the top of the list to receive genetic testing as part of my treatment plan. My mom was diagnosed in the 1980’s, before genetic testing was a standard of care, and before the CDH1 mutation was even discovered. In a way, it is good that I was tested before my mom, because she has since tested negative for all common breast cancer causing genes. If I would have known that previously, I may have felt a false sense of security and not been as diligent about finding answers to my own rare and aggressive cancer.


While going through the genetic testing process, I was expecting to test positive for one of the widely publicized BRCA genes. That is why it was a complete shock when the genetic counselor read my results, telling me I tested positive for a CDH1 mutation. Basically, this gene mutation significantly increases my chances of having lobular breast cancer, check, and what is known as hereditary diffuse gastric cancer (HDGC), check. HDGC is REALLY hard to detect due to the signet ring cells being present in the lining of the stomach in single cell or cluster formations, not forming tumors like more traditional cancer cells. There is no blood test, biopsy, procedure or scan that is guaranteed to detect these cells. Because of the difficulty in detection of HDGC, the current recommendation for cancer prevention is to have a prophylactic total gastrectomy (you read that correctly, the current recommendation is to have your entire stomach removed before you are diagnosed with cancer). As you can imagine, that was a tough pill to swallow after already having had both of my breasts removed less than six months ago and undergoing ten months of active treatment so far.


So, while undergoing treatment for breast cancer, I’ve been researching this mutation, found an amazing online support system through social media, and learned about a clinical study being conducted at the National Institute of Health (NIH) focusing on CDH1. I quickly enrolled, and was accepted into the study. I traveled to the NIH for my initial visit, met with the clinical team, endured numerous tests, and had my initial endoscopy with biopsies (stomach mapping) completed. I just learned that they found cancer cells in my stomach during the procedure. No one knows how fast this cancer progresses, and the five year survival rate for Stage IV HDGC, the stage when individuals tend to be diagnosed, is only about 4% (according to No Stomach for Cancer). This is why total gastrectomy is recommended in individuals diagnosed with the CDH1 mutation, because when cancer is found, it is usually too late. Once I wrap my mind around this new information, and speak with my oncologist, I will be scheduling my total gastrectomy as soon as possible. I am aware this procedure will completely alter my life, but I am also hoping it will save it.


Breast cancer at a young age is difficult, and having a rare genetic mutation on top of it does not make it any easier. I have found support through family, friends, pets, gardening, watching mindless television, engaging in support groups on social media, wonderful health care professionals, and blogging. So, although my urine remains toxic, and I can mark professional pill taker as a present occupation on my resume, I am hopeful that cancer does not have to be the last story I tell and that others can learn from what I am going through.

23 views0 comments

Recent Posts

See All

Comments


bottom of page